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- UBA1 : ubiquitin like modifier activating enzyme 1
- ISCU : iron-sulfur cluster assembly enzyme
- HADHB : hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
- COQ8B : coenzyme Q8B
- HADHA : hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
- GBE1 : 1,4-alpha-glucan branching enzyme 1
- COQ4 : coenzyme Q4
- COQ8A : coenzyme Q8A
- COQ6 : coenzyme Q6, monooxygenase
- COQ2 : coenzyme Q2, polyprenyltransferase
- HK1
- HLCS : holocarboxylase synthetase
- MMP21
- BLOC1S5
- PDXK
- LIPC : lipase C, hepatic type
- HPD : 4-hydroxyphenylpyruvate dioxygenase
- ALDOA
- GYS1 : glycogen synthase 1
- OAT : ornithine aminotransferase